Paediatrics: Cystic fibrosis: management (1)

Cystic fibrosis: management (1)

The management of the child with CF requires close co-operation be-tween local hospitals and regional centres. Patients and their families gain much from expert clinics, and from other patients and their families. Effective management requires a multidisciplinary team approach, which should include:

·  paediatric pulmonologist;

·  physiotherapist;

·  dietician;

·  nurse liaison or practitioner in CF;

·  primary care team;

·  teacher;

·  psychologist.

All patients with CF should have a thorough annual multisystem review. Table 9.1 summarizes the range of information that is needed. You will find following these parameters helpful when assessing progression, deteriora-tion, and need for supraregional referral for heart–lung transplantation.